Prastiya Indra Gunawan and Lusiana and Darto Saharso (2016) Hemispherectomy procedure in proteus syndrome. Iranian Journal of Child Neurology, 10 (3). pp. 86-90. ISSN 20080700

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Abstract

Proteus syndrome is a rare overgrowth disorder including bone, soft tissue, and skin. Central nervous system manifestations were reported in about 40% of the patients including hemimegalencephaly and the resultant hemicranial hyperplasia, convulsions and mental deficiency. We report a 1-month-old male baby referred to Pediatric Neurology Clinic Soetomo Hospital, Surabaya, Indonesia in 2014 presented recurrent seizures since birth with asymmetric dysmorphic face with the right side larger than the left, subcutaneous mass and linear nevi. Craniocervical MRI revealed hemimegalencephaly right cerebral hemisphere. Triple antiepileptic drugs were already given as well as the ketogenic diet, but the seizures persisted. The seizure then was resolved after hemispherectomy procedure.

Item Type:	Article
Uncontrolled Keywords:	ntractable epilepsy, Linear nevi, Hemimegalencephaly, Hemispherectomy, Proteus syndrome
Subjects:	R Medicine > R Medicine (General) R Medicine > RJ Pediatrics
Divisions:	01. Fakultas Kedokteran > Ilmu Kesehatan Anak (Sub Spesialis)
Creators:	Creators NIM Prastiya Indra Gunawan NIDN0729047602 Lusiana UNSPECIFIED Darto Saharso NIDN0010085002
Depositing User:	arys fk
Date Deposited:	16 Oct 2020 07:16
Last Modified:	16 Oct 2020 07:16
URI:	http://repository.unair.ac.id/id/eprint/100045
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